Sensorineural hearing impairment
A type of hearing impairment in one or both ears related to an abnormal functionality of the cochlear nerve.
Also called: Hearing loss, sensorineural, Sensorineural deafness, Sensorineural hearing loss.
Conditions associated with sensorineural hearing impairment
The following conditions have been associated with sensorineural hearing impairment in medical literature. This is informational and not a diagnosis.
1p36 deletion syndrome
1p36 deletion syndrome is a medical condition that may be associated with various symptoms and signs....
3-methylglutaconic aciduria type 8
3-methylglutaconic aciduria type 8 is a medical condition that may be associated with various symptoms and sig...
Adult-onset autosomal dominant leukodystrophy
Adult-onset autosomal dominant leukodystrophy is a medical condition that may be associated with various sympt...
Alobar holoprosencephaly
Alobar holoprosencephaly is a medical condition that may be associated with various symptoms and signs....
Alpha-mannosidosis, infantile form
Alpha-mannosidosis, infantile form is a medical condition that may be associated with various symptoms and sig...
Alport syndrome
Alport syndrome is a medical condition that may be associated with various symptoms and signs....
Alstrom syndrome
A multisystemic disorder characterized by cone-rod dystrophy, hearing loss, obesity, insulin resistance and hy...
Autosomal dominant Charcot-Marie-Tooth disease type 2A2
Autosomal dominant Charcot-Marie-Tooth disease type 2A2 is a medical condition that may be associated with var...
Autosomal dominant optic atrophy, classic form
Autosomal dominant optic atrophy, classic form is a medical condition that may be associated with various symp...
Autosomal dominant spastic paraplegia type 9A
Autosomal dominant spastic paraplegia type 9A is a medical condition that may be associated with various sympt...
Bilateral polymicrogyria
Bilateral polymicrogyria is a medical condition that may be associated with various symptoms and signs....
Biotinidase deficiency
Biotinidase deficiency is a medical condition that may be associated with various symptoms and signs....
Brown-Vialetto-van Laere syndrome 1
Any Brown-Vialetto-van Laere syndrome in which the cause of the disease is a mutation in the SLC52A3 gene....
Brown-Vialetto-van Laere syndrome 2
Any Brown-Vialetto-van Laere syndrome in which the cause of the disease is a mutation in the SLC52A2 gene....
CINCA syndrome
CINCA syndrome is a medical condition that may be associated with various symptoms and signs....
CODAS syndrome
Codas syndrome is a multiple congenital anomalies syndrome characterized by Cerebral, Ocular, Dental, Auricula...
Carey-Fineman-Ziter syndrome 1
A rare condition characterized by the association of hypotonia, Moebius sequence (bilateral congenital facial ...
Charcot-Marie-Tooth disease X-linked dominant 1
Charcot-Marie-Tooth neuropathy that is inherited in an X-linked manner, and is associated with mutation(s) in ...
Charcot-Marie-Tooth disease axonal type 2C
Autosomal dominant Charcot-Marie-Tooth disease type 2C (CMT2C) is a form of axonal Charcot-Marie-Tooth disease...
Charcot-Marie-Tooth disease type 1E
Charcot-Marie-Tooth disease type 1E is a medical condition that may be associated with various symptoms and si...
Charcot-Marie-Tooth disease type 1E
A rare subtype of CMT1 characterized by a variable clinical presentation. Onset within the first two years of ...
Charcot-Marie-Tooth disease type 1F
Charcot-Marie-Tooth disease type 1F is a medical condition that may be associated with various symptoms and si...
Charcot-Marie-Tooth disease type 4B2
Charcot-Marie-Tooth disease type 4B2 is a medical condition that may be associated with various symptoms and s...
Charcot-Marie-Tooth disease type 4C
Charcot-Marie-Tooth disease type 4C is a medical condition that may be associated with various symptoms and si...
Cockayne syndrome type 1
Cockayne syndrome caused by mutation(s) in the ERCC8 gene, encoding DNA excision repair protein ERCC-8....
Cockayne syndrome type 2
Cockayne syndrome caused by mutation(s) in the ERCC6 gene, encoding DNA excision repair protein ERCC-6....
Coffin-Siris syndrome 12
Coffin-Siris syndrome 12 is a medical condition that may be associated with various symptoms and signs....
Congenital myasthenic syndrome
Congenital myasthenic syndrome is a medical condition that may be associated with various symptoms and signs....
Cornelia de Lange syndrome 1
Any Cornelia de Lange syndrome in which the cause of the disease is a mutation in the NIPBL gene....
D-glyceric aciduria
A metabolic disorder characterized by D-glyceric acid excretion. It has been described in several patients. Cl...
DEGCAGS syndrome
DEGCAGS syndrome is a medical condition that may be associated with various symptoms and signs....
Distal renal tubular acidosis
Distal renal tubular acidosis is a medical condition that may be associated with various symptoms and signs....
Fabry disease
Fabry disease is a medical condition that may be associated with various symptoms and signs....
Facioscapulohumeral dystrophy
Facioscapulohumeral dystrophy is a medical condition that may be associated with various symptoms and signs....
Familial cold urticaria
Familial cold urticaria is a medical condition that may be associated with various symptoms and signs....
Folinic acid-responsive seizures
Folinic acid-responsive seizures is a medical condition that may be associated with various symptoms and signs...
Full NF2-related schwannomatosis
Full NF2-related schwannomatosis is a medical condition that may be associated with various symptoms and signs...
GATA2 deficiency spectrum
GATA2 deficiency spectrum is a medical condition that may be associated with various symptoms and signs....
Generalized arterial calcification of infancy
Generalized arterial calcification of infancy is a medical condition that may be associated with various sympt...
Granulomatosis with polyangiitis
Granulomatosis with polyangiitis is a medical condition that may be associated with various symptoms and signs...
Tests providers may use to investigate sensorineural hearing impairment
When investigating sensorineural hearing impairment, a healthcare provider may order one or more of the following laboratory tests. Test selection is a clinical decision made by a qualified professional.
CBC with Differential
Measures red blood cells, white blood cells, and platelets to help evaluate overall health and detect disorder...
Comprehensive Metabolic Panel (CMP)
Measures 14 substances in the blood to assess kidney and liver function, electrolyte balance, and blood sugar ...
Fasting Glucose
Measures blood sugar after fasting to screen for diabetes and prediabetes....
Hemoglobin A1c (HbA1c)
Reflects average blood sugar over the past 2-3 months....
Magnesium
Measures magnesium levels, important for nerve and muscle function....
Thyroid Panel
Comprehensive thyroid testing including TSH, free T4, and free T3....
Urinalysis
Examines urine content to help detect urinary tract infections, kidney disease, and diabetes....
Symptoms commonly seen alongside sensorineural hearing impairment
Dysphagia
Difficulty in swallowing....
Fatigue
A subjective feeling of tiredness characterized by a lack of energy and motivation....
Fever
Body temperature elevated above the normal range....
Headache
Cephalgia, or pain sensed in various parts of the head, not confined to the area of distribution of any nerve....
Muscle weakness
Reduced strength of muscles....
Seizure
A seizure is an intermittent abnormality of nervous system physiology characterized by a transient occurrence ...
When to seek care
Seek care from a qualified healthcare provider if sensorineural hearing impairment is severe, persistent, worsening, or accompanied by concerning symptoms. If you think you have a medical emergency, call your local emergency number immediately.
Frequently Asked Questions
What does the symptom sensorineural hearing impairment mean?
Sensorineural hearing impairment is a health sign or symptom described in medical literature. A type of hearing impairment in one or both ears related to an abnormal functionality of the cochlear nerve.
Which conditions are associated with sensorineural hearing impairment?
Sensorineural hearing impairment has been reported in association with 136 conditions in the medical literature we index, including 1p36 deletion syndrome, 3-methylglutaconic aciduria type 8, Adult-onset autosomal dominant leukodystrophy, Alobar holoprosencephaly, Alpha-mannosidosis, infantile form. These associations do not mean you have any of these conditions.
Should I see a doctor about sensorineural hearing impairment?
You should discuss any persistent or concerning symptoms with a qualified healthcare provider. This website does not provide diagnosis. If you have severe symptoms or signs of a medical emergency, seek care immediately.